The septal leaflet is typically larger than normal.
The conduction system is usually displaced downward into the ventricle.
Right ventricle dilitation is associated with a decreased number of myocardial fibers.
The anterior leaflet in left-sided Ebstein's anomaly is usually large.
Associated atrial septal defects are uncommon
Question 2: Which of the following statements is true regarding the clinical presentation of Ebstein's anomaly?
The lesion is more common in females.
Up to 50% of patients diagnosed in infancy will not survive past 2 years of age.
Palpitations are unusual except in the setting of WPW.
Cyanosis at birth indicates fixed RVOTO in these patients.
The majority of patients do not have a decline in their functional NHYA class.
Question 3: Which of the following statements is true regarding operative management of Ebstein's anomaly?
Elective repair should be delayed in all patients until functional status deteriorates to NYHA class III or IV.
Small associated atrial septal defects should be closed by simple suture.
Short papillary muscles on the anterior leaflet do not preclude valve repair.
Sutures should be placed on the ventricular side of coronary sinus during valve replacement to avoid injury to the conduction system.
Question 4: Which of the following statements is true for results following operative repair of Ebstein's anomaly?
Late death from congestive heart failure is common.
Reoperation for tricuspid insufficiency is more common following valve repair than for valve replacement.
Maximal exercise testing demonstrates improved oxygen uptake but little increase in exercise duration.
The majority of patients will remain in class I or II at long-term followup.
Question 1 Question 2 Question 3 Question 4 Question 1 Question 2 Question 3 Question 4