TAPVC occurs when established connections between the lungs and heart atrophy and disappear.
All anomalous pulmonary venous drainage must connect with the right atrium.
The most common type of TAPVC is cardiac.
Ventricular septal defect is the most common associated anomaly in patients with TAPVC.
Anomalous drainage to the azygous vein is classified as supracardiac.
Question 2: Which of the following statements is true regarding the clinical presentation of TAPVC?
Survival is dependent on the amount of left-to-right shunting.
Severe cyanosis and distress indicates severe pulmonary venous obstruction rather than pulmonary hypertension.
Severe pulmonary venous obstruction is most likely to occur in patients with supracardiac TAPVC.
Infants with non-obstructed TAPVC can be expectantly managed.
All patients should have prompt catheterization to delineate the anatomy of TAPVC.
Question 3: Which of the following statements is true regarding operative management of TAPVC?
Separate implantation of each pulmonary vein to the left atrium provides the most reliable reconstruction.
A secundum ASD can be closed with simple suture in these patients.
The azygous vein can be mobilized and anastomosed directly to the left atrium in this type of supracardiac TAPVC.
The coronary sinus can be unroofed into the left atrium to correct cardiac TAPVC.
Ligation of the vertical vein during infracardiac TAPVC repair should be done immediately prior to discontinuing CPB.
*** Note: questions for the Cor Triatriatum section coming soon.... ***
Question 1 Question 2 Question 3 Question 1 Question 2 Question 3