Review of Surgical Experience in 188 Infants and Young Children with Ebstein’s Anomaly

This single institution study retrospectively reviewed the outcome of pediatric Ebstein’s anomaly surgical correction. Of the 188 patients with a median (IQR) age of three years (1.6–5.6), 108 had cone reconstruction. Nearly 30 percent of patients required a bidirectional cavopulmonary shunt. Another 12 percent developed recurrent moderate to severe tricuspid regurgitation (TR). There was a lower incidence of recurrent TR in the group undergoing cone reconstruction. The age group of patients did not appear to affect the incidence of recurrent TR, reoperation, or death.