Anomalous origin of the left coronary artery from the pulmonary artery (ALCAPA) is a rare congenital anomaly that is one of the most common causes of myocardial ischemia and infarction in children. If untreated, it results in a mortality rate of up to 90% within the first year of life. In the current era, establishment of a two coronary artery system is considered the goal for repair of ALCAPA.
ALERT!
This site is not optimized for Internet Explorer 8 (or older).
Please upgrade to a newer version of Internet Explorer or use an alternate browser such as Chrome or Firefox.
Congenital
March 21, 2013
March 21, 2013
The Aortic Translocation procedure was introduced for the management of patients with complex transposition of the great arteries (TGA) with a ventricular septal defect (VSD) and pulmonary stenosis (PS). The technique has proven especially useful in the subset of patients with anatomic variables that complicate the performance of a Rastelli repair.
March 21, 2013
The completion Fontan operation is, as the name implies, the final stage of palliation for patients who have had previous surgery to address various types of single ventricle congenital heart disease.
March 21, 2013
The superior cavopulmonary anastomosis is the first of two operations used in a staged Fontan approach for definitive palliation of functionally single ventricle hearts.
March 17, 2013
By Robert H. Anderson, MD, FRCPath
Introductory Remarks
March 17, 2013
In this last video in the series, we examine three specimens with rarer lesions associated with congenitally corrected transposition. The first is an example of a heart with discordant atrioventricular, but concordant ventriculo-arterial connections.
March 17, 2013
In the second videoclip exploring congenitally corrected transposition, we show a specimen in which the potentially corrected circulatory patterns are uncorrected to a degree by the presence of a ventricular septal defect.
March 17, 2013
In one-third of patients with congenitally corrected transposition, there can be co-existing pulmonary stenosis. As explained, although it is stated that no heart exists in the Idriss archive with this lesion, this is not the case, and such a heart in shown in the next video clip.
March 17, 2013
We first demonstrate the key features of congenitally corrected transposition, namely the discordant connections across both the atrioventricular and ventriculo-arterial junctions. The two discordant connections cancel each other out, so that potentially the circulations are congenitally corrected.
