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Congenital Portal
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This video presents the case of a seven-month-old boy with large subaortic ventricular septal defect (VSD) and a moderate degree of aortic valve (AV) regurgitation due to aortic valve cusp prolapse... More
March 21, 2013
The “sutureless” neoatrium technique was initially described for anastomotic stenosis occurring after repair of total anomalous pulmonary venous connection (post-repair pulmonary vein stenosis, PRPVS). The procedure is also helpful in patients with congenital pulmonary vein stenosis and has been used in selected patients on the initial presentation of total anomalous pulmonary venous connection.
March 21, 2013
The surgical management of patients with tetralogy of Fallot and significant right ventricular outflow tract obstruction (RVOTO) remains controversial. The authors describe the use of a monocusp in patients with right ventricular outflow tract obstruction.
March 21, 2013
Anomalous origin of the left coronary artery from the pulmonary artery (ALCAPA) is a rare congenital anomaly that is one of the most common causes of myocardial ischemia and infarction in children. If untreated, it results in a mortality rate of up to 90% within the first year of life. In the current era, establishment of a two coronary artery system is considered the goal for repair of ALCAPA.
March 17, 2013
In the second videoclip exploring congenitally corrected transposition, we show a specimen in which the potentially corrected circulatory patterns are uncorrected to a degree by the presence of a ventricular septal defect.
March 17, 2013
In one-third of patients with congenitally corrected transposition, there can be co-existing pulmonary stenosis. As explained, although it is stated that no heart exists in the Idriss archive with this lesion, this is not the case, and such a heart in shown in the next video clip.
March 17, 2013
We first demonstrate the key features of congenitally corrected transposition, namely the discordant connections across both the atrioventricular and ventriculo-arterial junctions. The two discordant connections cancel each other out, so that potentially the circulations are congenitally corrected.
March 17, 2013
By Robert H. Anderson, MD, FRCPath
Introductory Remarks
March 17, 2013
In this last video in the series, we examine three specimens with rarer lesions associated with congenitally corrected transposition. The first is an example of a heart with discordant atrioventricular, but concordant ventriculo-arterial connections.
March 6, 2013
Editors Note
Patient Selection