Transposition of the Great Arteries With Intact Ventricular Septum and Type 1 Aortopulmonary Window

Objectives

Aortopulmonary window is a rare form of congenital heart disease that can be seen in isolation or with associated other complex cardiac lesions. Although aortopulmonary window has been associated with other complex cardiac lesions, only a few cases of this condition associated with transposition of the great arteries with an intact ventricular septum have been reported in the literature.

Methods

The authors demonstrate the successful repair of transposition of the great arteries with an associated aortopulmonary window in a neonate.

Results

The repair consisted of an arterial switch operation and repair of the aortopulmonary window.

Conclusion

Timing of surgical intervention for an aortopulmonary window depends on its size and location, as well as the associated complex congenital heart lesion. Repair of transposition of the great arteries in association with an aortopulmonary window can be successfully achieved in the neonatal period, with excellent outcomes.

This educational content was originally presented during the STSA 64th Annual Meeting. This content is published with the permission of the STSA. For more information on the STSA and its next Annual Meeting, please click here.