This site is not optimized for Internet Explorer 8 (or older).

Please upgrade to a newer version of Internet Explorer or use an alternate browser such as Chrome or Firefox.

Repair of Type 2 Aortopulmonary Window in an Infant with Right Aortic Arch

Tuesday, November 16, 2021

Ergün S, Çoban Ş, Can A, Kaygın MA. Repair of Type 2 Aortopulmonary Window in an Infant With Right Aortic Arch. November 2021. doi: 10.25373/ctsnet.17026817

A two-month-old female presented with failure to thrive and shortness of breath during feedings. Echo images show ed type 2 aortopulmonary window, left ventricular enlargement, and systemic pulmonary hypertension. After a median sternotomy, the mean, right, and left pulmonary arteries, and ascending aorta were dissected. There was no patent ductus arteriosus. The AP window was visualized. The ascending aorta was then cannulated distally. Next, the right atrium was cannulated. Then the left heart was vented via right superior pulmonary vein. Next, the aortic cross-clamp was applied, and the heart was arrested with the Del Nido cardioplegic solution.  

The aortotomy was then performed, and the AP window was visualized between the posteromedial wall of the ascending aorta and pulmonary bifurcation. It was quite close to the right aortic arch. The AP window was closed with glutaraldehyde-treated autologous pericardium and 7-0 Prolene sutures. Then we checked the patch for any residual shunt by removing the pulmonary arterial snares.  

To finish the procedure, the aortotomy was closed after de-airing and the patient was weaned from cardiopulmonary bypass easily. The pulmonary arterial pressure was measured. The postoperative echo demonstrated an intact wall between the aorta and pulmonary arteries. The patient was extubated on postoperative day four and discharged on postoperative day eight. 


  1. Mori K, Ando M, Takao A, Ishikawa S, Imai Y. Distal type of aortopulmonary window.Report of 4 cases. Br Heart J. 1978 Jun;40(6):681–9.
  2. Tiraboschi R, Salomone G, Crupi G, Manasse E, Salim A, Carminati M, et al. Aortopulmonary window in the first year of life: Report on 11 surgical cases. Ann Thorac Surg. 1988;46:438–41.
  3. Richardson JV, Doty DB, Rossi NP, Ehrenhaft JL. The spectrum of anomalies of aortopulmonary septation. J Thorac Cardiovasc Surg. 1979;78:21–7.
  4. Berry TE, Bharati S, Muster AJ, Idriss FS, Santucci B, Lev M, et al. Distal aortopulmonary septal defect, aortic origin of the right pulmonary artery, intact ventricular septum, patent ductus arteriosus and hypoplasia of the aortic isthmus: A newly recognized syndrome. Am J Cardiol. 1982;49:108–16.


The information and views presented on represent the views of the authors and contributors of the material and not of CTSNet. Please review our full disclaimer page here.

Add comment

Log in or register to post comments