Surgical Repair in Coexisting Transposition of the Great Arteries With Infracardiac Total Anomalous Pulmonary Connection

Cardiac surgeons frequently encounter transposition of the great arteries (TGA) and total anomalous pulmonary venous connection (TAPVC). Coexisting transposition of the TGA and TAPVC is a rare combination, with the infracardiac variety being even rarer. So far, only seven cases have been described in literature with combined infracardiac TAPVC and TGA, with only one case being obstructed. 

The first successful anatomical correction was performed by Lopes et al. on a 22-hour-old infant with TGA and subdiaphragmatic TAPVC (1). Later, Seliem et al. reported a total anatomical correction in a four-year-old child with supra-cardiac type (2), and Mykychak et al. reported another case of total anatomical correction in an infracardiac type of TAPVC (3).  

In this video, the authors report on a four-month-old infant who had TGA and infracardiac TAPVC to discuss the operative strategy in this scenario. 

References

1. opes LM, Tavares GMP, Mailho FL, Almeida VDPCD, Mangione JA (2001) Echocardiographic diagnosis of transposition of the great arteries associated with anomalous pulmonary venous connection. Arq Bras Cardiol 77(1):66–68.
2. Seliem MA, Bouholaigah IH, Palileo MR (2004) Complete transposition of the great arteries and total anomalous pulmonary venous connection with a small atrial septal defect: a rare combination resulting in balanced pulmonary systemic circulations. Ann Saudi Med 24(2):133–135.
3. Mykychak Y, Fedevych O, Maksymenko A, Yemets I (2017) Simultaneous arterial switch and totally anomalous pulmonary venous connection repair in a 5-hour-old child, complicated by pulmonary venous stenosis. Interact Cardiovasc Thorac Surg 24(5):809–810. https:// doi. org/ 10. 1093/icvts/ ivw452.

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