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Congenital - Cyanotic

March 17, 2017
Three quarters of a century in caring for patients with congenital heart disease are summarized well in this brief viewpoint article, with the big data issue discussed.
January 10, 2017
A comprehensive discussion on an important parameter for cardiologists and surgeons dealing with congenital and structural / valve disease, as applicable to the systemic circulation 
November 23, 2016
In this single institution retrospective study, the relationship of PA pressure to long-term mortality was assessed in patients undergoing unifocalization for pulmonary atresia with VSD.  A mean PA intraoperative pressure > 25mm Hg was associated with worse survival, and was the sole predictor of medium-term death.
November 23, 2016
A single institution experience during 22 years for early repair of complete AV canal defects (CAVCD) is reported.  Repair was performed in 159 pts between 8 and 12 weeks of age.   Operative mortality was 1.9% and later mortality was 7.7%.  13% required reoperation during long-term follow-up, primarily for left AV valve regurgitation.  Left AV valve
July 12, 2016
This video shows the reconstruction of the pulmonary artery in an 8-year-old girl, who had undergone repair of truncus arteriosus at the age of one.
June 4, 2016
In order to develop an algorithm for identifying acute deterioration (urgent intubation or cardiopulmonary resuscitation) in infants with parallel systemic and pulmonary circulation, continuous physiologic monitoring data of 25 patients were retrospecitively reviewed and analyzed.  20 events were identified in 13 infants.  The algorithm was effective
April 12, 2016
Results of an audit of the National Congenital Heart Disease database were evaluted to determine characteristics of patients undergoing reoperation within 30 days of their primary procedure.  Among over 18,000 patients, 3.5% had early reoperations.  The reoperations were most commonly arterial shunt, PA band, and VSD procedures.  60 day mortality was
March 7, 2016
This retrospective study of 434 infants and children undergoing TOF repair focused on how methods of handling hypoplastic pulmonary arteries affects long-term outcomes.  The most agressive patching technique resulted in the highest incidence of reintervention, whereas patients who had no intervention for hypoplastic pulmonary arterties had the lowest
January 30, 2016
The authors determined the need for transannular patch enlargement (TAPE) in management of ToF by measuring the ratio between pulmonary annulus size to aortic valve annulus size (GA ratio).  A retrospective analysis of 122 pts who had undergone ToF repair with or without TAPE was performed.  GA ratios were smaller in patients undergoing TAPE.  The GA
September 7, 2015
This video presents the case of a 37-year-old man diagnosed with tetralogy of Fallot (TOF) with absent pulmonary valve syndrome.