The authors present a successful surgical treatment in a 14-year-old girl with Loeys-Dietz syndrome; a redo aortic arch and ascending aorta replacement with a valve-sparing operation was performed.
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Congenital - Acyanotic
November 14, 2017
October 17, 2017
The authors report a rare patient with complete Cantrell’s pentalogy associated with a left ventricular diverticulum, who underwent an uncomplicated full repair.
October 13, 2017
The authors report on the design and use of a growth-accommodating device that may have a variety of pediatric applications, including valve annuloplasty. The device consists of a biodegradable core and a tubular braided sleeve (woven much like a 'finger trap' toy).
August 17, 2017
Jimmy Kimmel's son was born with Tetralogy of Fallot with pulmonary atresia. He had emergency surgery at the Children’s Hospital Los Angeles in the first week of his life, and this video describes the operation and he goes on to thank all the medical staff who helped in the baby's care. This video has had 11 million hits.
May 17, 2017
Surgery for treatment of this aortopathy entailing aortic root replacement was assessed in this single institution retrospective study of 34 children. 90% had valve sparing surgery; there was no operative mortality. Reintervention is commonly needed, and frequent surveillance imaging is recommended.
March 17, 2017
Three quarters of a century in caring for patients with congenital heart disease are summarized well in this brief viewpoint article, with the big data issue discussed.
November 23, 2016
In this single institution retrospective study, the relationship of PA pressure to long-term mortality was assessed in patients undergoing unifocalization for pulmonary atresia with VSD. A mean PA intraoperative pressure > 25mm Hg was associated with worse survival, and was the sole predictor of medium-term death.
November 23, 2016
A single institution experience during 22 years for early repair of complete AV canal defects (CAVCD) is reported. Repair was performed in 159 pts between 8 and 12 weeks of age. Operative mortality was 1.9% and later mortality was 7.7%. 13% required reoperation during long-term follow-up, primarily for left AV valve regurgitation. Left AV valve
September 6, 2016
This video describes the technique of right ventricular papillary muscle approximation to the septum (RV-PMA) as an adjunct to cone reconstruction of Ebstein’s anomaly, and reviews some of the authors’ initial results.
August 10, 2016
This video illustrates a no-patch closure for complete atrioventricular canal defects.