This is a single stage, midline complete repair of pulmonary atresia with ventricular septal defect, major aortopulmonary collaterals, and absent intrapericardial native pulmonary arteries.
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Pulmonary valve disease (congenital)
One-Stage Midline Unifocalization With Complete Repair of Pulmonary Atresia, Ventricular Septal Defect, and Major Aortopulmonary Collaterals
June 29, 2020
November 20, 2019
In this study from the Mayo Clinic, outcomes of bioprosthetic valves placed in the pulmonary position in adults with congenital heart disease were evaluated. Cumulative prosthetic valve dysfunction at 15 years was 48%, raising the question of the efficacy of using such valves in this position.
Abnormal Pulmonary Artery Bending Correlates With Increased Right Ventricular Afterload Following the Arterial Switch Operation
October 2, 2019
Abnormal pulmonary artery bending in the setting of the Lecompte maneuver may affect right ventricular afterload in the absence of stenosis.
September 23, 2019
The authors demonstrate the implantation of a prosthetic valve in the pulmonary position using a left anterior thoracotomy on an empty beating heart.
July 3, 2019
Bauser-Heaton and colleagues evaluated outcomes for patients with complex tetralogy of Fallot with pulmonary atresia and major aortopulmonary collateral arteries (MAPCAs), focusing on those patients who underwent unifocalization with placement of a shut rather than simultaneous intracardiac repair.
June 25, 2019
This is a cohort study from the Pediatric Cardiac Care Consortium based on data from 616 patients with pulmonary atresia with intact ventricular septum (PA/IVS) treated between 1982 and 2003. Median follow-up was 16.7 years (IQR 12.6-22.7).
Novel Approach to Repair of Tetralogy of Fallot With Absent Pulmonary Valve Syndrome and Severe Airway Compression
June 5, 2019
The authors present a new approach to relieving severe airway compression in tetralogy of Fallot with absent pulmonary valve and massively dilated pulmonary arteries.
Bileaflet Polytetrafluoroethylene Conduits for Right Ventricular Outflow Tract Reconstruction in Small Children
October 22, 2018
Bicuspid-valved polytetrafluoroethylene conduits are an excellent choice for right ventricular outflow tract reconstruction in patients aged less than two years.
Symptomatic Tetralogy of Fallot in Young Infants: Primary Repair or Shunt—Pediatric Health Information System Database Analysis
September 18, 2018
This study compares the early outcomes and hospital charges associated with early primary repair vs systemic-to-pulmonary artery shunt for neonates and young infants.
September 6, 2018
The Nikaidoh procedure is a useful technique for patients with complex transposition of the great arteries.