Content from the Journal of the American Neurological Surgeons.

PTFE Monocusp Valve for RVOT Reconstruction

Patient Selection The surgical management of patients with tetralogy of Fallot and significant right ventricular outflow tract obstruction (RVOTO) remains controversial.  For patients who have a congenitally small pulmonary valve annulus who are not candidates for a valve-sparing repair, there have historically been two options: (1) transannular patch or (2) valved conduit insertion.  The advantage…

“Sutureless” Pulmonary Vein Stenosis Repair

Patient Selection The “sutureless” neoatrium technique was initially described for anastomotic stenosis occurring after repair of total anomalous pulmonary venous connection (post-repair pulmonary vein stenosis, PRPVS).  The procedure is also helpful in patients with congenital pulmonary vein stenosis and has been used in selected patients on the initial presentation of total anomalous pulmonary venous connection. …

Brom Aoroplasty for Supravalvar Aortic Stenosis

Brom’s three-patch aortoplasty is indicated for the repair of supravalvar aortic stenosis, which can occur as an isolated defect or as a part of Williams syndrom.  This syndrome is characterized by supravalvar aortic stenosis, elfin craniofacial features, peripheral pulmonary artery stenosis, and hypercalcemia.  Patient Selection Brom’s three-patch aortoplasty is indicated for the repair of supravalvar…

Aortic Translocation for TGA with VSD and PS

Editor Note Patient Selection This procedure was introduced for the management of patients with complex transposition of the great arteries (TGA) with a ventricular septal defect (VSD) and pulmonary stenosis (PS).  The technique has proven especially useful in the subset of patients with anatomic variables that complicate the performance of a Rastelli repair, which include:…

Discordant Atrioventricular Connections 1: Congenitally Corrected Transposition

We first demonstrate the key features of congenitally corrected transposition, namely the discordant connections across both the atrioventricular and ventriculo-arterial junctions. The two discordant connections cancel each other out, so that potentially the circulations are congenitally corrected. In the heart shown in this videoclip, the septal structures are intact, so that indeed the circulations are…

Discordant Atrioventricular Connections 2: Congenitally Corrected Transposition with Ventricular Septal Defect

In the second videoclip exploring congenitally corrected transposition, we show a specimen in which the potentially corrected circulatory patterns are uncorrected to a degree by the presence of a ventricular septal defect. More than half the patients with congenitally corrected transposition have deficient ventricular septation, and as in the heart shown, most usually the defects…